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Gewählte Publikation:

STOGMANN, W; KERL, H; SCHMIDBERGER, H.
Lipoid dermatoarthritis (multicentric reticulohistiocytosis) (author's transl)
EUR J PEDIAT. 1975; 121(1): 71-80. Doi: 10.1007/BF00464396 (- Case Report)
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Co-Autor*innen der Med Uni Graz
Kerl Helmut
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Abstract:
The case of a 10-year-old girl with an infrequently observed lipid dermatoarthritis is reported. This is a systemic disease of unknown etiology characterized by a nodular eruption of the skin, mucosa and synovia, resulting in destructive arthritis and disfigurement of the facies. Biopsy of a nodule, whether from skin or synovia, discloses a cellular infiltrate consisting of histiocytes and multinucleated giant cells with lipid inclusions. No effective treatment is known.
Find related publications in this database (using NLM MeSH Indexing)
Arthritis - complications Arthritis - pathology
Child -
Chronic Disease -
Female -
Glycoproteins - analysis
Histiocytes -
Humans -
Hydrarthrosis - complications
Lipids - analysis
Phospholipids - analysis
Skin Diseases - complications Skin Diseases - pathology
Synovial Membrane - pathology

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