Medizinische Universität Graz Austria/Österreich - Forschungsportal - Medical University of Graz
Gewählte Publikation:
Fruhwirth, J; Mischinger, HJ; Werkgartner, G; Beham, A; Pfaffenthaller, EC.
Köhlmeier-Degos's disease with primary intestinal manifestation.
Scand J Gastroenterol. 1997; 32(10):1066-1070
Doi: 10.3109/00365529709011226
(- Case Report)
Web of Science
PubMed
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- Führende Autor*innen der Med Uni Graz
- Fruhwirth Johannes
- Co-Autor*innen der Med Uni Graz
- Beham Alfred
- Mischinger Hans-Jörg
- Werkgartner Georg
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- Abstract:
- Disseminated intestinal and cutaneous thromboangiitis (synonyms: Köhlmeier-Degos's syndrome, malignant atrophic papulosis, progressive arterial mesenterial vascular occlusive disease) is a rare, systemic vascular disease that is mainly manifested in the skin, gastrointestinal tract, and nervous system. The disease first appears as a necrotizing papulous dermatosis; as it generalizes, infarcted necroses develop in internal organs. These ischemic complications are the reason for the usually fatal outcome of the disease. A case report of a primary intestinal manifestation of this disease illustrates the clinical course, diagnosis, histopathologic findings, and differential diagnosis, with consideration of the current literature. Deposits of acid mucopolysaccharides and humoral immune mechanisms appear to play a role in the etiology and pathogenesis of this usually fatal vascular disease.
- Find related publications in this database (using NLM MeSH Indexing)
- Humans -
- Intestinal Diseases - etiology
- Male -
- Middle Aged -
- Skin Diseases, Papulosquamous - complications
- Skin Diseases, Vascular - complications
- Syndrome -
- Thromboangiitis Obliterans - complications
- Find related publications in this database (Keywords)
- Disseminated Intestinal and Cutaneous Thromboangiitis
- Kohlmeier-Degoss Disease