Medizinische Universität Graz Austria/Österreich - Forschungsportal - Medical University of Graz
Gewählte Publikation:
SHR Neuro Krebs Kardio Lipid Stoffw Microb
Gamillscheg, A; Zobel, G; Spuller, E; Reiterer, F; Beitzke, A.
Aortic coarctation associated with alveolar capillary dysplasia and misalignment of the pulmonary veins.
Pediatr Cardiol. 2008; 29(1):191-194
Doi: 10.1007/s00246-007-9063-5
(- Case Report)
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- Führende Autor*innen der Med Uni Graz
- Gamillscheg Andreas
- Co-Autor*innen der Med Uni Graz
- Beitzke Albrecht
- Reiterer Friedrich
- Spuller Ekkehard
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- Abstract:
- After surgical repair of an aortic coarctation a term infant presented with severe pulmonary hypertension and cyanosis unresponsive to treatment including extracorporeal membrane oxygenation. The atypical clinical course became apparent once the accompanying diagnosis of congenital alveolar capillary dysplasia with misalignment of the pulmonary veins had been established at autopsy. In infants with congenital heart defects and with refractory pulmonary hypertension unexplainable on anatomic findings, a lung biopsy at the time of cardiac repair should be considered to avoid further therapies that would not alter the uniformly fatal course of this rare lung disorder.
- Find related publications in this database (using NLM MeSH Indexing)
- Aortic Coarctation - epidemiology
- Dilatation, Pathologic -
- Extracorporeal Membrane Oxygenation -
- Fatal Outcome -
- Female -
- Humans -
- Infant, Newborn -
- Lymphatic Vessels - pathology
- Persistent Fetal Circulation Syndrome - etiology
- Pulmonary Alveoli - pathology
- Pulmonary Veins - abnormalities