Medizinische Universität Graz Austria/Österreich - Forschungsportal - Medical University of Graz
Gewählte Publikation:
SHR Neuro Krebs Kardio Lipid Stoffw Microb
Urban, C; Benesch, M; Sovinz, P; Schwinger, W; Lackner, H.
Fatal Evans' syndrome after matched unrelated donor transplantation for hyper-IgM syndrome.
EUR J HAEMATOL. 2004; 72(6): 444-447.
Doi: 10.1111/j.1600-0609.2004.00256.x
(- Case Report)
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- Führende Autor*innen der Med Uni Graz
- Benesch Martin
- Urban Ernst-Christian
- Co-Autor*innen der Med Uni Graz
- Lackner Herwig
- Ritter-Sovinz Petra
- Schwinger Wolfgang
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- Abstract:
- A 3 and 1/2-yr-old boy underwent matched unrelated stem cell transplantation (SCT) for hyper-IgM syndrome. He developed acute and chronic skin graft-vs.-host disease (GVHD). Ten months following SCT he presented with severe hemolytic anemia and thrombocytopenia (Evans' syndrome). Treatment included high-dose steroids, intravenous immunoglobulins, cyclosporine, mycophenolate mofetil, chemotherapeutic agents (cyclophosphamide, vincristine, VP-16), immunoadsorption, and anti-CD20 and anti-CD52 monoclonal antibodies without response. The patient died 16 months after SCT.
- Find related publications in this database (using NLM MeSH Indexing)
- Anemia, Hemolytic, Autoimmune - drug therapy
- Blood Donors - drug therapy
- Fatal Outcome - drug therapy
- Graft vs Host Disease - etiology
- Hematopoietic Stem Cell Transplantation - adverse effects
- Humans - adverse effects
- Immunoglobulin M - adverse effects
- Immunologic Deficiency Syndromes - complications
- Immunosuppressive Agents - therapeutic use
- Infant - therapeutic use
- Male - therapeutic use
- Skin Diseases - etiology
- Syndrome - etiology
- Thrombocytopenia - drug therapy
- Treatment Failure - drug therapy
- Find related publications in this database (Keywords)
- Evans' syndrome
- hyper-IgM syndrome
- stem cell transplantation