Medizinische Universität Graz Austria/Österreich - Forschungsportal - Medical University of Graz
Gewählte Publikation:
Beitzke, A; Zobel, G; Rigler, B; Stein, JI; Suppan, C.
Scimitar syndrome with absence of the right pulmonary artery: a case with volume-induced, reversible, left-sided pulmonary hypertension.
Pediatr Cardiol. 1992; 13(2):119-121
Doi: 10.1007/BF00798220
(- Case Report)
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- Führende Autor*innen der Med Uni Graz
- Beitzke Albrecht
- Co-Autor*innen der Med Uni Graz
- Rigler Bruno
- Stein Joerg-Ingolf
- Zobel Gerfried
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- Abstract:
- An infant with scimitar syndrome, absent right pulmonary artery, and systemic blood supply to the right lung presented in severe cardiac failure. Cardiac catheterization revealed suprasystemic pressure of the left pulmonary artery and a high pulmonary vascular resistance. Right-sided pneumonectomy abolished cardiac failure and normalized both pulmonary artery pressure and resistance. Pure volume load affecting one lung--as in this case through absence of the right pulmonary artery plus additional left-to-right shunt from a systemic collateral--can lead to pulmonary hypertension. Early operative intervention can reverse this process and prevent pulmonary vascular disease.
- Find related publications in this database (using NLM MeSH Indexing)
- Angiocardiography -
- Blood Volume - physiology
- Female - physiology
- Heart Catheterization - physiology
- Hemodynamic Processes - physiology
- Humans - physiology
- Hypertension, Pulmonary - physiopathology
- Infant - physiopathology
- Pneumonectomy - physiopathology
- Postoperative Complications - physiopathology
- Pulmonary Artery - abnormalities
- Scimitar Syndrome - physiopathology