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Böck, K; Pschaid, C; Topakian, R; Stieglbauer, K; Doppler, S; von Oertzen, JT; Pichler, R.
Mononeuritis multiplex: association with infectious condition and familial background in a tropical environment: a case report.
Wien Klin Wochenschr. 2014; 126 Suppl 1(4):S42-S45 Doi: 10.1007/s00508-014-0504-x (- Case Report)
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Co-Autor*innen der Med Uni Graz
Pichler Robert
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Abstract:
Mononeuritis multiplex is characterized by an asymmetric pattern with affection of the peripheral nervous system; this form of polyneuropathy is often seen in non-systemic vasculitis. We present a case of multiplex neuropathy in a patient with histologicaly verified Hailey-Hailey disease. With the exception of this comorbidity--in its characteristic form presenting additionally with a superinfected subdermal node--we did not find any other possible etiologic factor possibly causative of multiplex neuritis. The diagnosis was confirmed by electrophysiological testing. To our knowledge, this is the first case report indicating a possible relationship between Hailey-Hailey disease and multiplex neuritis. There exists only one related study in the literature, which was conducted in Columbia--our patient's home country. This study delineates a clinically similar dermal disease (pemphigus foliaceus) in patients from rural Colombia (El Bagre). The authors detected anti-neuronal antibodies which were interpreted to be responsible for the pathognomonic burning sensations.
Find related publications in this database (using NLM MeSH Indexing)
Adult -
Analgesics - therapeutic use
Anti-Inflammatory Agents - therapeutic use
Anti-Inflammatory Agents -
Anti-Inflammatory Agents -
Humans -
Male -
Mononeuropathies - diagnosis
Mononeuropathies - drug therapy
Mononeuropathies - genetics
Pemphigus, Benign Familial - diagnosis
Pemphigus, Benign Familial - drug therapy
Pemphigus, Benign Familial - genetics
Treatment Outcome -
Tropical Climate -

Find related publications in this database (Keywords)
Polyneuropathy
Mononeuritis multiplex
Hailey-Hailey disease
Pemphigus foliaceus
Vasculitis
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