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SHR Neuro Cancer Cardio Lipid Metab Microb

Ott, I; Weber, M; Gattenlohner, S; Schwager, K; Hagen, R; Baier, G.
Multifocal manifestation of Rosai-Dorfman disease. A rare case of purely extranodal sinus histiocytosis in the elderly
J APPL ELECTROCHEM. 2010; 40(4): 263-267. Doi: 10.1007/s00106-008-1861-4
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Co-authors Med Uni Graz
Gattenlöhner Stefan
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Abstract:
Rosai-Dorfman disease belongs to the group of childhood histiocytoses and was initially described as sinus histiocytosis with massive lymphadenopathy. Its rare purely extranodal manifestation is primarily found in the head and neck region. An atypical primary manifestation in an elderly patient with multifocal extranodal disease is described, and this pathological entity is reviewed. Specific difficulties concerning differential diagnostic aspects as well as individually appropriate treatment strategies are discussed.

Find related publications in this database (Keywords)
Histiocytosis
Multifocal
Rosai-Dorfman disease
Extranodal sinus histiocytosis
Paranasal sinus tumor
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